What is the survival rate of tricuspid atresia?

Tricuspid atresia (TA) is the third most common cyanotic congenital cardiac lesion, with a mortality rate of 90% before the age of 10 years. Surgical intervention has reduced the mortality, but with unfavourable anatomy the mortality remains high.

Is tricuspid atresia compatible with life?

Although treatment greatly improves the outcome for babies with tricuspid atresia, complications can develop later in life, including: Formation of blood clots that can lead to a clot blocking an artery in the lungs (pulmonary embolism) or cause a stroke.

How serious is tricuspid atresia?

Tricuspid atresia occurs when this valve doesn’t form at all, and no blood can go from the right atrium through the right ventricle to the lungs for oxygen. Because a baby with tricuspid atresia may need surgery or other procedures soon after birth, this birth defect is considered a critical congenital heart defect.

Is tricuspid atresia common?

It is the third most common cyanotic congenital heart defect; the other 2 frequently observed cyanotic congenital cardiac anomalies are transposition of the great arteries and tetralogy of Fallot. Tricuspid atresia is the most common cause of cyanosis with left ventricular hypertrophy.

How often does tricuspid atresia occur?

Tricuspid atresia is a congenital heart defect, occurring in two out of every 10,000 live births. Relatively rare, it accounts for about 1 to 2 percent of all cases of congenital heart disease.

Is tricuspid atresia genetic?

Most of the occurrences of tricuspid atresia that were identified with a genetic cause occurred as part of a multitude of congenital heart diseases. Genetic culprits ranged from extra chromosomes and chromosomal deletions to SNPs. The involvement of some genes such as ZFPM2 and NKX2-5 is certain.

What kind of heart disease is tricuspid atresia?

Tara Karamlou MD, MSc, in Critical Heart Disease in Infants and Children (Third Edition), 2019 Tricuspid atresia (TA) is a type of cyanotic congenital heart defect (CCHD) characterized by complete obstruction of the atrioventricular valve associated with the morphologic right ventricle.

Where does the blood go in a baby with tricuspid atresia?

In babies with tricuspid atresia, the tricuspid valve that controls blood flow from the right atrium to the right ventricle is not formed, so blood is unable to get to the right ventricle and out to the lungs.

Where is the VSD located in tricuspid atresia?

The VSD is located between the left and the right ventricles. This allows blood to flow from the left ventricle to the pulmonary artery in the right ventricle. In some newborns with tricuspid atresia, a fetal vessel called the ductus arteriousus stays open to allow blood to circulate to the lungs from the aorta.

Is there a patent foramen Oval for tricuspid atresia?

Tricuspid atresia is a cyanotic congenital cardiac anomaly which is characterised by agenesis of the tricuspid valve and right ventricular inlet. There is almost always an obligatory intra-atrial connection through either an ASD or patent foramen ovale (PFO) in order for circulation to be complete 5.