Why do cystic fibrosis patients need high-calorie diet?

Individuals with cystic fibrosis require more energy to breathe normally, fight lung infections and compensate for poor digestion. For these reasons, they need more calories than people without CF.

What diet modifications are required for cystic fibrosis?

Whether eating at home or away, here are some simple tips:

• Drink whole milk and milkshakes.
• Add extra butter or olive oil to foods like potatoes or pasta.
• Use regular (not diet) dressings on salads or vegetables.
• Eat burgers with bacon and cheese.
• Eat pizza with extra cheese.
• Add cheese to sandwiches.

What type of diet should a child with cystic fibrosis be on?

Like other children, those with CF should eat a balanced diet that includes whole grains, fruits and vegetables, dairy products, and protein. High-fat, high-calorie foods and snacks; foods with extra salt and low in sugar, can benefit children and teens with CF.

How many calories should a cystic fibrosis patient eat?

The webcast below highlights the following information: Women with CF should consume 2,500 calories a day to maintain their weight and 3,000 calories a day to gain weight. Men with CF should consume 3,000 calories a day to maintain their weight and up to 3,700 calories a day to gain weight.

What are the most common nutritional consequences of cystic fibrosis?

Nutrition Implications of Cystic Fibrosis

• very salty skin.
• persistent coughing, at times with phlegm.
• frequent lung infections.
• wheezing or shortness of breath.
• poor growth/weight gain in spite of a good appetite.
• frequent greasy, bulky stools or difficulty in bowel movements.
• high blood sugar.
• kidney stones.

Why can’t CF patients gain weight?

The sticky mucus from cystic fibrosis can block normal absorption of key nutrients and fat in the intestines, causing: poor digestion. slow growth. trouble gaining weight.

Can you be fat and have cystic fibrosis?

Overweight/obesity is common in adults with CF. 25% of adults with CF who have severe mutations are overweight or obese. Overweight/obese patients with CF are more likely to have hypertension. Overweight/obesity is associated with better pulmonary function.

What triggers cystic fibrosis?

Cystic fibrosis is caused by a change, or mutation, in a gene called CFTR (cystic fibrosis transmembrane conductance regulator). This gene controls the flow of salt and fluids in and out of your cells. If the CFTR gene doesn’t work the way it should, a sticky mucus builds up in your body.

Can you drink alcohol if you have cystic fibrosis?

Alcohol may aggravate or intensify health conditions common to people with CF such as dehydration, osteoporosis, and liver disease. Drinking alcohol can increase the likelihood of pancreatitis, a painful inflammation of the pancreas.

Why are people with cystic fibrosis skinny?

Many people envy the slender ones with cystic fibrosis who have pancreatic insufficiency, which is characteristic of about 85 percent of CF cases. That insufficiency makes it difficult to digest food and absorb nutrients, like fat and protein.

What kind of diet do you need for cystic fibrosis?

Energy needs of people with CF are estimated to be 1 ½ to 2 times the needs of those without CF. A high-calorie, high-fat diet, with 40 percent of total calories from fat is generally recommended. 1

How much calories do you need for cystic fibrosis?

People with CF typically need up to twice the amount of daily calories as others who are of similar age and weight. To gain weight, you will need to take in about an extra 500 calories a day. Spend some time thinking about what your weight gain goal should be.

What is the relationship between nutrition and cystic fibrosis?

Nutritional status has a clear relationship with disease outcomes, and malnutrition in CF is typically a result of chronic negative energy balance secondary to malabsorpti … Optimal nutrition support has been integral in the management of cystic fibrosis (CF) since the disease was initially described.

What are the clinical practice guidelines for cystic fibrosis?

This document includes recommendations in the following areas: routine surveillance for pulmonary disease, therapeutics, and nutritional and gastrointestinal care. Early nutritional intervention and monitoring for respiratory and gastrointestinal disease in infants with cystic fibrosis (CF) is vital to improve long-term outcomes.